Von hippel lindau disease icd 9

von hippel lindau disease icd 9

Other hamartoses, not elsewhere classified

  • 2015
  • Billable Thru Sept 30/2015
  • Non-Billable On/After Oct 1/2015

  • ICD-9-CM 759.6 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 759.6 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM. 759.6 converts approximately to:
  • 2015/16 ICD-10-CM Q85.8 Other phakomatoses, not elsewhere classified
  • Angiomatosis of meninges
  • Astrocytic hamartoma
  • Cerebellar hemangioblastomatosis
  • Congenital erector pili hamartoma
  • Congenital hamartoma
  • Congenital hamartoma of skin
  • Congenital hamartosis
  • Congenital leptomeningeal angiomatosis
  • Cowden syndrome
  • Dermal connective tissue hamartoma
  • Diffuse smooth muscle hamartoma
  • Eccrine angiomatous hamartoma
  • Epidermal nevus
  • Epidermolytic epidermal nevus
  • Fat-storing hamartoma of dermal dendrocytes
  • Fibrolipomatous hamartoma of nerve
  • Hairy malformation of palms and soles
  • Hamartoma
  • Hamartoma of apocrine sweat gland apparatus
  • Hamartoma of eccrine sweat gland apparatus
  • Hamartoma of hypothalamus
  • Hamartoma of integument
  • Hamartoma of muscle
  • Hamartoma of pilosebaceous apparatus
  • Hamartoma of pituitary and hypothalamus
  • Hamartoma of retina
  • Hamartoma of skin
  • Hamartoma of skin appendage
  • Hereditary neurocutaneous angiomata
  • Lhermitte-Duclos disease
  • Lipomatous hamartoma
  • Moniliform hamartoma
  • Neoplasm and/or hamartoma
  • Neurocutaneous melanosis sequence
  • Parkes Weber syndrome
  • Peutz-Jeghers polyps of small bowel
  • Peutz-Jeghers syndrome
  • Retinal hamartoma
  • Riley-Smith syndrome
  • Spinal hamartoma
  • Splenic hamartoma
  • Sturge-Weber syndrome
  • Von Hippel-Lindau syndrome
  • A group of neurocutaneous disorders manifested by facial and leptomeningeal angiomas, ipsilateral gyriform calcifications of the cerebral cortex, seizures, development delay, hemiplegia, emotional and behavioral problems, and glaucoma and other ocular disorders. Nevus flammeus on the side of the face ipsilateral to angiomatosis sometimes extends to neck, chest, and back. Angiomatosis may

    occasionally involve the choroid plexus, thyroid, pituitary gland, lungs, gastrointestinal organs, pancreas, ovaries, and thymus. Correlation between the distribution of the nevus and the course of the trigeminal nerve is responsible for naming the syndrome "trigemino-encephalo-angiomatosis," but later findings found the relationship to be fortuitous. The syndrome frequently occurs in incomplete forms, presenting different combinations of symptoms

  • A rare inherited disorder in which blood vessels grow abnormally in the eyes, brain, spinal cord, adrenal glands, or other parts of the body. People with von hippel-lindau syndrome have a higher risk of developing some types of cancer
  • An inherited condition characterized by generalized hamartomatous multiple polyposis of the intestinal tract. Transmitted in an autosomal dominant fashion, peutz-jeghers syndrome consistently involves the jejunum and is associated with melanin spots of the lips, buccal mucosa, and fingers. This syndrome is associated with abnormalities of chromosome 19. Also known as jeghers-peutz syndrome and peutz's syndrome
  • An inherited familial cancer syndrome which is characterized by development of capillary hemangioblastomas of the central nervous system and retina; clear cell renal carcinoma; pheochromocytoma; pancreatic tumors; and inner ear tumors. The syndrome is associated with germline mutations of the vhl tumor suppressor gene, located on chromosome 3p25-26. Symptoms of vhl syndrome may not be apparent until the third decade of life. Cns hemangioblastoma is the most common cause of death, followed by clear cell renal cell carcinoma
  • Autosomal dominant disorder associated with cerebellar and retinal neoplasms; the most common manifestations are neurologic deficits associated with intracranial hemangioblastomas which may hemorrhage, causing ataxia, intracranial hypertension, and other signs of neurologic dysfunction
  • Syndrome:
    • Peutz-Jeghers
    • Sturge-Weber (-Dimitri)
    • von Hippel-Lindau

ICD-9-CM Volume 2 Index entries containing back-references to 759.6 :

Category: Disease

Similar articles: